Carnitine deficiency in lysinuric protein intolerance: Lysine-sparing effect of carnitine
In: The Tohoku Journal of Experimental Medicine, Jg. 153 (1987), S. 331-334
Online
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Zugriff:
Plasma carnitine deficiency (41% of normal control) was found in a 9 year-old boy with lysinuric protein intolerance. Following oral carnitine administration, the plasma level of lysine as well as carnitine has significantly increased (p less than 0.05). His well-being seemed to have improved on this substitutive remedy. Hitherto unrevealed these findings on LPI indicate that carnitine has a lysine-sparing effect and suggest that there might be a biosynthetic pathway of carnitine directly from free lysine in human.
| Titel: |
Carnitine deficiency in lysinuric protein intolerance: Lysine-sparing effect of carnitine
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| Autor/in / Beteiligte Person: | Goto, Atsuko ; Komatsu, Kazuo ; Takada, Goro ; Goto, Ryoji |
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| Zeitschrift: | The Tohoku Journal of Experimental Medicine, Jg. 153 (1987), S. 331-334 |
| Veröffentlichung: | Tohoku University Medical Press, 1987 |
| Medientyp: | unknown |
| ISSN: | 1349-3329 (print) ; 0040-8727 (print) |
| DOI: | 10.1620/tjem.153.331 |
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